A fatal presentation of dermatomyositis with facial swelling

Nishant Dwivedi, Christie Michael, D. Betty Lew, Sandra Arnold, Masanori Igarashi, Tulio Bertorini, Jerome W. Thompson, Linda Myers, Monica Brown

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Juvenile dermatomyositis (JDM) is the most common inflammatory autoimmune myopathy in children. Most common presentations consist of heliotrophic rash and/or gottron's papules in addition to proximal muscle weakness. A typical presentations have been reported. We present a 13-year-old African American male who presented with a two-week history of bilateral periorbital edema that was unresponsive to glucocorticoids. He had elevated transaminases but no detectable muscle weakness. A muscle biopsy was consistent with juvenile dermatomyositis. This case highlights the need to consider dermatomyositis in cases of facial swelling and the use of aggressive immunosuppressive therapies due to its associated vasculopathies.

Original languageEnglish (US)
Pages (from-to)745-749
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume76
Issue number5
DOIs
StatePublished - May 1 2012

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Dermatomyositis
Muscle Weakness
Myositis
Immunosuppressive Agents
Transaminases
Exanthema
African Americans
Glucocorticoids
Edema
Biopsy
Muscles
Juvenile dermatomyositis
Therapeutics

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Otorhinolaryngology

Cite this

A fatal presentation of dermatomyositis with facial swelling. / Dwivedi, Nishant; Michael, Christie; Lew, D. Betty; Arnold, Sandra; Igarashi, Masanori; Bertorini, Tulio; Thompson, Jerome W.; Myers, Linda; Brown, Monica.

In: International Journal of Pediatric Otorhinolaryngology, Vol. 76, No. 5, 01.05.2012, p. 745-749.

Research output: Contribution to journalArticle

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