Common pulmonary vein atresia

Report of three cases and review of the literature

Michael Perez, T. K.Susheel Kumar, Mario Briceno-Medina, Mohammed Alsheikh-Ali, Shyam Sathanandam, Christopher J. Knott-Craig

Research output: Contribution to journalReview article

1 Citation (Scopus)

Abstract

Common pulmonary vein atresia is a rare and usually fatal congenital anomaly, in which the pulmonary veins come together to form a confluence that does not connect to the left atrium. We report our experience with three cases of common pulmonary vein atresia and review the literature on this anomaly. The diagnosis of common pulmonary vein atresia must be entertained in any newborn that presents with cyanosis, refractory acidosis, and decreased systemic perfusion within the first 48 hours of life. Echocardiography is a useful screening tool, but cardiac catheterisation is the preferred diagnostic tool. Common pulmonary vein atresia can be fatal without surgical intervention, but survival after surgery continues to be poor.

Original languageEnglish (US)
Pages (from-to)629-635
Number of pages7
JournalCardiology in the Young
Volume26
Issue number4
DOIs
StatePublished - Apr 1 2016

Fingerprint

Pulmonary Atresia
Pulmonary Veins
Cyanosis
Cardiac Catheterization
Acidosis
Heart Atria
Echocardiography
Perfusion

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

Cite this

Perez, M., Kumar, T. K. S., Briceno-Medina, M., Alsheikh-Ali, M., Sathanandam, S., & Knott-Craig, C. J. (2016). Common pulmonary vein atresia: Report of three cases and review of the literature. Cardiology in the Young, 26(4), 629-635. https://doi.org/10.1017/S1047951115002334

Common pulmonary vein atresia : Report of three cases and review of the literature. / Perez, Michael; Kumar, T. K.Susheel; Briceno-Medina, Mario; Alsheikh-Ali, Mohammed; Sathanandam, Shyam; Knott-Craig, Christopher J.

In: Cardiology in the Young, Vol. 26, No. 4, 01.04.2016, p. 629-635.

Research output: Contribution to journalReview article

Perez, M, Kumar, TKS, Briceno-Medina, M, Alsheikh-Ali, M, Sathanandam, S & Knott-Craig, CJ 2016, 'Common pulmonary vein atresia: Report of three cases and review of the literature', Cardiology in the Young, vol. 26, no. 4, pp. 629-635. https://doi.org/10.1017/S1047951115002334
Perez, Michael ; Kumar, T. K.Susheel ; Briceno-Medina, Mario ; Alsheikh-Ali, Mohammed ; Sathanandam, Shyam ; Knott-Craig, Christopher J. / Common pulmonary vein atresia : Report of three cases and review of the literature. In: Cardiology in the Young. 2016 ; Vol. 26, No. 4. pp. 629-635.
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