Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis

On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group

Research output: Contribution to journalReview article

15 Citations (Scopus)

Abstract

Background: Patients with Hirschsprung disease are at risk for Hirschsprung-associated enterocolitis (HAEC), an inflammatory disorder of the bowel that represents the leading cause of serious morbidity and death in these patients. The diagnosis of HAEC is made based on clinical signs and symptoms which are often non-specific, making it difficult to establish a definitive diagnosis in many patients. The purpose of this guideline is to present a rational, expert-based approach to the diagnosis and management of HAEC. Methods: The American Pediatric Surgical Association Board of Governors established a Hirschsprung Disease Interest Group. Group discussions, literature review, and expert consensus were then used to summarize the current state of knowledge regarding diagnosis, management, and prevention of Hirschsprung-associated enterocolitis (HAEC). Results: Guidelines for the diagnosis of HAEC and its clinical grade, utilizing clinical history, physical examination findings, and radiographic findings, are presented. Treatment guidelines, including patient disposition, diet, antibiotics, rectal irrigations and surgery, are presented. Conclusions: Clear, standardized definitions of Hirschsprung-associated enterocolitis and its treatment are lacking in the literature. This guideline serves as a first step toward standardization of diagnosis and management. Level of evidence: V.

Original languageEnglish (US)
Pages (from-to)517-521
Number of pages5
JournalPediatric Surgery International
Volume33
Issue number5
DOIs
StatePublished - May 1 2017

Fingerprint

Enterocolitis
Guidelines
Hirschsprung Disease
Public Opinion
Signs and Symptoms
Physical Examination
Pediatrics
Anti-Bacterial Agents
Diet
Morbidity
Therapeutics

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Surgery

Cite this

On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group (2017). Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis. Pediatric Surgery International, 33(5), 517-521. https://doi.org/10.1007/s00383-017-4065-8

Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis. / On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group.

In: Pediatric Surgery International, Vol. 33, No. 5, 01.05.2017, p. 517-521.

Research output: Contribution to journalReview article

On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group 2017, 'Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis', Pediatric Surgery International, vol. 33, no. 5, pp. 517-521. https://doi.org/10.1007/s00383-017-4065-8
On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group. Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis. Pediatric Surgery International. 2017 May 1;33(5):517-521. https://doi.org/10.1007/s00383-017-4065-8
On behalf of the American Pediatric Surgical Association Hirschsprung Disease Interest Group. / Guidelines for the diagnosis and management of Hirschsprung-associated enterocolitis. In: Pediatric Surgery International. 2017 ; Vol. 33, No. 5. pp. 517-521.
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