Superficial siderosis due to a lumbar ependymoma mimicking adult-onset spinocerebellar ataxia

Konstantinos Spengos, Sofia Vassilopoulou, Georgios Tsivgoulis, Georgios Karachalios, Demetris Vassilopoulos

Research output: Contribution to journalArticle

10 Citations (Scopus)

Abstract

Superficial siderosis (SS), as a result of chronic subarachnoid haemorrhage and haemosiderin deposition on the leptomeninges and subpial layers of the brain, cerebellum and spinal cord, can cause ataxia, pyramidal tract lesions and hearing deficits. In cases with not pronounced hearing impairment adult-onset spinocereballar ataxia can be considered as a differential diagnostic alternative. We report a similar case where the diagnosis of SS was established by means of gradient echo MRI sequences 5 years after symptom onset. A bleeding lumbar ependymoma was identified as a source of haemorrhage. Surgical tumor resection stopped any further disease progression. Our report underlines that clinicians should be aware of the clinical features and diagnostic pitfalls of SS. Time of diagnosis and neurosurgical intervention can essentially influence the patients' prognosis.

Original languageEnglish (US)
Pages (from-to)705-707
Number of pages3
JournalClinical Neurology and Neurosurgery
Volume109
Issue number8
DOIs
StatePublished - Oct 1 2007
Externally publishedYes

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Siderosis
Spinocerebellar Ataxias
Ependymoma
Ataxia
Hemorrhage
Hemosiderin
Pyramidal Tracts
Subarachnoid Hemorrhage
Hearing Loss
Cerebellum
Hearing
Disease Progression
Spinal Cord
Brain
Neoplasms

All Science Journal Classification (ASJC) codes

  • Surgery
  • Clinical Neurology

Cite this

Superficial siderosis due to a lumbar ependymoma mimicking adult-onset spinocerebellar ataxia. / Spengos, Konstantinos; Vassilopoulou, Sofia; Tsivgoulis, Georgios; Karachalios, Georgios; Vassilopoulos, Demetris.

In: Clinical Neurology and Neurosurgery, Vol. 109, No. 8, 01.10.2007, p. 705-707.

Research output: Contribution to journalArticle

Spengos, Konstantinos ; Vassilopoulou, Sofia ; Tsivgoulis, Georgios ; Karachalios, Georgios ; Vassilopoulos, Demetris. / Superficial siderosis due to a lumbar ependymoma mimicking adult-onset spinocerebellar ataxia. In: Clinical Neurology and Neurosurgery. 2007 ; Vol. 109, No. 8. pp. 705-707.
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